Cystic fibrosis (CF) is a genetic disease that causes the formation of very thick mucus in the lungs, digestive tract and other organs. This phenomenon is caused by the disorder at the level of ion exchange membrane between the inner and outer environment of the cell. Is mainly due to the accumulation of chloride in sweat, which is one of the major manifestations of cystic fibrosis. Hence there is general naming diagnoses as "salty children."
Thick mucus secretion reduces pancreatic enzymes, which are important for the digestion of food and the availability of important nutrients from food (such as vitamins, minerals and trace elements). People with untreated CF often suffer from malnutrition. Good nutritional status is an important prognostic factor, mainly due to delay in pulmonary complications. Inadequate nutrition causes growth retardation, susceptibility to infectious diseases, physical and mental weakness. The main instruments for achieving proper nutrition is a regular high-calorie diet, adequate substitution of pancreatic enzymes, adequate nutritional support.
The main reason for poor digestion is insufficient production of pancreatic enzymes (digestive enzymes that are produced in the pancreas), undigested food accumulates in the intestine and becomes a breeding ground for various bacteria. Formed abdominal pain, cramps and bloating. Nutritional requirements of patients with CF are much more demanding than for healthy individuals. Sufficient intake of fats, essential fatty acids, proteins, sugars, probiotics, and not least of vitamins is essential for a good prognosis.